Beyond Breathless: Unravelling The Enigma Of Pulmonary Arteriovenous Malformations

Authors

Sri Mounya Jampala, JSS Medical CollegeFollow
Jagadish Kumar K Dr., JSS ACADEMY OF HIGHER EDUCATION AND RESEARCHFollow
Manjunath V G, JSS Medical CollegeFollow
Nandish H R, JSS Medical College, JSSAHERFollow

Author ORCID Identifier

https://orcid.org/0009-0007-2366-4343

Abstract

Pulmonary Arteriovenous Malformations (AVMs) are abnormal connections between the pulmonary arteries and veins, leading to a direct shunting of blood without passing through the normal capillary bed. These AVMs can be associated with a rare genetic disorder called Hereditary Hemorrhagic Telangiectasia (HHT), also known as Osler-Weber-Rendu syndrome. HHT is an autosomal dominant disorder characterized by the development of fragile telangiectasias in various organs, including the skin and mucous membranes. These telangiectasias are prone to bleeding, leading to recurrent nosebleeds and mucocutaneous bleeding. In patients with HHT, the most common site of AVMs is in the lungs. Pulmonary AVMs can cause significant health risks due to the right-to-left shunting of blood, leading to hypoxemia and possible complications like stroke, cerebral abscesses, and heart failure.

Publication Date

2023

Publisher

JSS Academy of Higher Education & Research

First Page

114

Last Page

120

Keywords

Pulmonary Arteriovenous Malformations, Hereditary Hemorrhagic Telangiectasia, CT Pulmonary Angiography, Clubbing

Word Count

780

Recommended Citation

Jampala S, K JK Dr., V G M, H R N. Beyond Breathless: Unravelling The Enigma Of Pulmonary Arteriovenous Malformations. Digital Journal of Clinical Medicine. 2023; 5(3): 114-120. doi: https://doi.org/10.55691/2582-3868.1145

Creative Commons License

This work is licensed under a Creative Commons Attribution-Noncommercial-No Derivative Works 4.0 License.